Khan, JavedSykes, David2018-06-202014Khan, Javed, and David B Sykes. 2014. “Case Report: a 37-Year-Old Male with Telangiectasias, Polycythemia Vera, Perinephric Fluid Collections, and Intrapulmonary Shunting.” BMC Hematology 14 (1) (July 22). doi:10.1186/2052-1839-14-11.2052-1839http://nrs.harvard.edu/urn-3:HUL.InstRepos:37137075The TEMPI syndrome was recently described in 2011, and is characterized by the constellation of five hallmarks: Telangiectasias, Erythrocytosis and elevated Erythropoietin, Monoclonal gammopathy, Perinephric fluids collections, and Intrapulmonary shunting. The underlying pathophysiology is unknown, though it has been postulated that the monoclonal gammopathy may play a causal role.en-USErythrocytosis,ErythropoietinMonoclonal gammopathyPerinephric fluidPolycythemiaTEMPIJournal Article2017-06-0920142018-06-2010.1186/2052-1839-14-11