Publication:
The mouse C9ORF72 ortholog is enriched in neurons known to degenerate in ALS and FTD

Thumbnail Image

Open/View Files

Date

2014

Published Version

Journal Title

Journal ISSN

Volume Title

Publisher

The Harvard community has made this article openly available. Please share how this access benefits you.

Research Projects

Organizational Units

Journal Issue

Citation

Suzuki, Naoki, Asif Maroof, Florian T Merkle, Kathryn Koszka, Atsushi Intoh, Ian Armstrong, Rob Moccia, Brandi N Davis-Dusenbery, and Kevin Eggan. 2014. “The mouse C9ORF72 ortholog is enriched in neurons known to degenerate in ALS and FTD.” Nature neuroscience 16 (12): 1725-1727. doi:10.1038/nn.3566. http://dx.doi.org/10.1038/nn.3566.

Research Data

Abstract

Using transgenic animals harboring a targeted LacZ insertion, we studied the expression pattern of the C9ORF72 mouse ortholog. Unlike most genes mutated in ALS, which are ubiquitously expressed, the C9ORF72-ortholog was most highly transcribed in the neuronal populations sensitive to degeneration in ALS and FTD. Thus, our study provides a potential explanation for the cell type specificity of neuronal degeneration caused by C9ORF72 mutations.

Description

Keywords

Amyotrophic lateral sclerosis (ALS), frontotemporal dementia (FTD), C9ORF72, motor neuron, cortical neuron, hippocampus, astrocyte, microglial

Terms of Use

This article is made available under the terms and conditions applicable to Other Posted Material (LAA), as set forth at Terms of Service

Endorsement

Review

Supplemented By

Referenced By

Related Stories